Hypertrophic Pachymeningitis from Neuro-Behçet’s Disease: A Case Report
Keywords:
Optic Neuritis, Pachymeningitis, Behçet’s DiseaseAbstract
A 26-year-old female presented with visual loss for 10 days from optic neuritis, which had recurred in the fellow eye one year apart. Neuroimaging, Pathergy test and skin biopsy results supported the diagnosis of neuro-Behçetʼs disease. The patient was successfully treated with pulse methylprednisolone followed by prednisolone and immunosuppressive agents.
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Hatano N, Behari S, Nagatani T, et al. Idiopathic hypertrophic cranial pachymeningitis: clinicoradiological spectrum and therapeutic options. Neurosurgery. 1999; 45(6):1336-42.
Siva A, Saip S. The spectrum of nervous system involvement in Behcetʼs syndrome and its differential diagnosis. J Neurol. 2009;256(4):513-29.
Yoon BN, Kim SJ, Lim MJ, et al. Neuro-Behçetʼs Disease Presenting as Hypertrophic Pachymen-ingitis. Exp Neurobiol. 2015;24(3):252-5.
Alkan G, Kartal A, Emiroğlu M, Paksoy Y. Neuro-Behçet disease presented with pachymeningitis in a child. Arch Argent Pediatr. 2019;117(6):e644-e647.
Behcetʼs disease: A report of three clinically distinct cases from North-west India. Indian Journal of Health Sciences and Biomedical Research (KLEU) 11(1): 89-91, Jan-Apr 2018. | DOI: 10.4103/kleuhsj.kleuhsj_150_17
Ohno S, Ohguchi M, Hirose S, Matsuda H, Wakisaka A, Aizawa M. Close association of HLA-Bw51 with Behçetʼs disease. Arch Ophthalmol. 1982;100:1455-8.
Takeno M. The association of Behçetʼs syndrome with HLA-B51 as understood in 2021. Curr Opin Rheumatol. 2022;34(1):4-9.
Karthik SN, Bhanu K, Velayutham S, Jawahar M. Hypertrophic pachymeningitis. Ann Indian Acad Neurol. 2011;14(3):203-4.
Nishio S, Morioka T, Togawa A, et al. Spontaneous resolution of hypertrophic cranial pachymeningitis. Neurosurg Rev. 1995;18(3):201-4.
Alpsoy E, Zouboulis C, Ehrlich GE. Mucocutaneous lesions of Behçetʼs disease. Yonsei Medical Journal. 2007;48(4):573-85.
Alpsoy E, Dönmez L, Bacanlı A, Apaydin C, Butun B. Review of the chronology of clinical manifestations in 60 patients with Behçetʼs disease. Dermatology. 2003;207(4):354-6.
Kalkan G, Karadag AS, Astarci HM, Akbay G, Ustun H, Eksioglu M. A histopathological approach: when papulopustular lesions should be in the diagnostic criteria of Behçetʼs disease? Journal of the European Academy of Dermatology and Venereology. 2009;23(9):1056-60.
Kalay Yildizhan İ, Boyvat A. Diagnostic Sensitivity of Different Applications of Pathergy Test for Behçetʼs Disease. Arch Rheumatol. 2019;35(1):29-34.
International Team for the Revision of the International Criteria for Behçetʼs Disease (ITRICBD). The International Criteria for Behҫetʼs Disease (ICBD): a collaborative study of 27 countrieson the sensitivity and specificity of the new criteria. J Eur AcadDermatol Venereol. 2014;28:338-47.
Hatemi G, Christensen R, Bang D, et al. 2018 update of the EULAR recommendations for the management of Behçetʼs syndrome. Ann Rheum Dis. 2018;77(6):808-18.
Hirohata S, Kikuchi H, Sawada T, et al. Analysis of various factors on the relapse of acute neurological attacks in Behçetʼs disease. Mod Rheumatol. 2014;24(6):961-5.
Hatemi G, Christensen R, Bang D, et al. 2018 update of the EULAR recommendations for the management of Behçetʼs syndrome. Ann Rheum Dis. 2018;77(6):808-18.
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